WHAT IS BID 4 BATTENS AND WHAT IS BATTEN DISEASE
What is Bid 4 Battens
Bid 4 Battens is a auction that raises awarness of Batten Disease and raises funds for the Batting for Battens Foundation to help set up a library of variety resouces for families to share. Bands from all over Australia (plus the Wallabies) have donated mechandise to be auction off on Ebay (Date TBA). Last year raised funds went towards a chair that raises and tilts electronically to aid a famliy lift their son. From this site you can view before hand what items that will be up for auction by using the menu on the side. And this we have a little something special donated by the ARU a fully signed wallibies jersey.
What is Batten Disease
Batten Disease is rarely diagnosed immediately and is often mistaken for epilepsy, retardation, retinitis pigmentosa, even schizomophrenia in adults. An opthalmologist can observe pathological changes in the retina. This often provides one of the first diagnostic clues. Onset is characterised by begining vision loss. Seizures, clumsiness and personality and behavoural changes. Batten Disease causes continuing physical and metal deterioration, leading to death.
It is a recessive inherited disease, meaning baoth parents must carry the same gene. A child must inherit a copy of the bad gene from both parents in order to be affected. A child that inherits a bad copy from just one parent will be a carrier.
The group of disease known as Batten disease or the Neuronal Ceroid lipofuscinoses (NCL) are progressive degenerative, genetic metabolic diseases that occur in children and in adults. The condition is named after the british paediatrician who first described it in 1903. Batten Disease is relaively rare occurring in about 1 in 30,000 Births. The illness leads to a progressive deterioration of the brain and nervous system. Although thier understanding of Batten Disease is improving all the time, there is at pressent no cure or treatment that has any significant impact on the inexorable decline in bodily functions and inevitable early death.
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